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Treatments for Wilsons disease (hepatolenticular degeneration)
INFORMATIVE 
Tags: Wilsons disease, autosomal recessive, hereditary disease, heterozygous, neurological, treatments
This disease is treated with lifelong use of chelating agents known as D-penicillamine or trientine hydrochloride, drugs that help remove copper from tissue.
| | This disease is treated with lifelong use of chelating agents known as D-penicillamine or trientine hydrochloride, drugs that help remove copper from tissue. |
| | Patients will also need to take vitamin B6 and follow a low-copper diet, which means avoiding mushrooms, nuts, chocolate, dried fruit, liver, and shellfish. |
| | Consuming extra zinc may be helpful in blocking the intestines' absorption of copper. |
| | Liver transplantation is effective in patients with fulminant Wilson's disease that does not respond to the usual treatment. |
| | Because the primary defect resides within the liver, the transplantation is curative, but as it is only undertaken in severely ill patients the prognosis is still mediocre. |
Lister:
BobbysWorld
Source:
Compiled by LAL Editor
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